neurocutaneous 03

Topic: Pathology

Created on Friday, February 13 2009 by gliageek

Last modified on Friday, February 13 2009.

 
        A) Von Hippel-Lindau
 
        B) Neurofibromatosis, type 1
 
        C) Neurofibromatosis, type 2
 
        D) Cowden diseaae
 
        E) Tuberous sclerosis
 

 

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This question was created on February 13, 2009 by gliageek.
This question was last modified on February 13, 2009.

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

ANSWERS AND EXPLANATIONS

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A) von Hippel-Lindau

This answer is incorrect.

Hemangioblastomas are most closely associated with vHL.  (See References)

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B) Neurofibromatosis, type 1

This answer is incorrect.

Within the CNS, pilocytic astrocytomas of the optic nerve and chiasm are most closely associated with NF1  (See References)

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C) Neurofibromatosis, type 2

This answer is incorrect.

Schwannomas, menigiomas, and ependymomas characterize NF2  (See References)

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D) Cowden diseaae

This answer is incorrect.

Dysplastic gangliocytoma of the cerebellum (L'hermitte-Duclos disease) represents the CNS manifestation of Cowden disease  (See References)

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E) Tuberous sclerosis

This answer is correct.

Subependymal giant cell tumors are one of the cardinal manifestations of tuberous sclerosis.  (See References)

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References:

1. Graham, D.I., and Lantos, P.L. (2002). Greenfield's Neuropathology, 7th ed. Arnold Press, New York. (ISBN:0340742313)

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pathology
neurocutaneous 03
Question ID: 021309212
Question written by gliageek. (C) FrontalCortex.com 2006-2009, all rights reserved. Created: 02/13/2009
Modified: 02/13/2009
Estimated Permutations: 120