Neurocutaneous 06

Topic: Pathology

Created on Monday, February 16 2009 by gliageek

Last modified on Monday, February 16 2009.

 
        A) Neurofibromatosis, type 2
 
        B) Schwannomatosis
 
        C) Sturge-Weber disease
 
        D) Neurofibromatosis, type 1
 
        E) Von Hippel-Lindau disease
 

 

	= Go back to the top of the page.
	= Reload a different version of this question ().
	= Load a random question from the database.
	= Use this question as a template to create a totally NEW question.
	= Enter detailed rating for this question!
	= How users like you have rated this question.

This question was created on February 16, 2009 by gliageek.
This question was last modified on February 16, 2009.

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

ANSWERS AND EXPLANATIONS

---

A) Neurofibromatosis, type 2

This answer is correct.

For reasons which are not at all clear, meningioangiomatosis in NF2 is nearly always asymptomatic, even when multiple  (See References)

Please log in if you want to rate questions.

 

 

 

 

 

 

 

 

 

---

B) Schwannomatosis

This answer is incorrect.

Does not include meningioangiomatosis  (See References)

Please log in if you want to rate questions.

 

 

 

 

 

 

 

 

 

---

C) Sturge-Weber disease

This answer is incorrect.

SWD shows meningeal angiomatosis with associated cortical calcification  (See References)

Please log in if you want to rate questions.

 

 

 

 

 

 

 

 

 

---

D) Neurofibromatosis, type 1

This answer is incorrect.

Meningioangiomatosis is NOT part of NF1, although included as part of VRD in older literature (before molecular separation of NF1 and NF2)  (See References)

Please log in if you want to rate questions.

 

 

 

 

 

 

 

 

 

---

E) von Hippel-Lindau disease

This answer is incorrect.

Meningeal hemangioblastoma may be seen in vHLD  (See References)

Please log in if you want to rate questions.

 

 

 

 

References:

1. Love, S., Louis, D.N., and Ellison, D.W. (2008). Greenfield's Neuropathology, 8th Edition. Oxford University Press, USA (ISBN:0340906820)

Advertising:

Please log in if you want to rate questions.

 

FrontalCortex.com -- Neurology Review Questions -- Neurology Boards -- Board Review -- Residency Inservice Training Exam -- RITE Exam Review
pathology
Neurocutaneous 06
Question ID: 021609113
Question written by gliageek. (C) FrontalCortex.com 2006-2009, all rights reserved. Created: 02/16/2009
Modified: 02/16/2009
Estimated Permutations: 120